Fibrocystic Diseases of the Liver
In recent years there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis,...
| Corporate Author: | |
|---|---|
| Other Authors: | , |
| Format: | Electronic |
| Language: | English |
| Published: |
Totowa, NJ :
Humana Press,
2010.
|
| Series: | Clinical Gastroenterology
|
| Subjects: | |
| Online Access: | https://ezaccess.library.uitm.edu.my/login?url=http://dx.doi.org/10.1007/978-1-60327-524-8 |
Table of Contents:
- Preface
- A. Pathophysiology & Development. 1. Embryology and development of the ductal plate. 2. Cholangiocyte biology as relevant to cystic liver diseases. 3. Cholangiocyte cilia and basal bodies. 4. Genetics of fibrocystic diseases of the liver and molecular approaches to therapy
- B. Diagnosis. 5. Radiologic findings in the fibrocystic diseases. 6. Pathology of fibrocystic diseases of the liver
- C. Disease States. 7. Alagille syndrome and JAGGED1/NOTCH sequence. 8. Biliary atresia and the ductal plate. 9. Nephronopthisis and Renal-hepatic-pancreatic dysplasia of Ivemark. 10. Meckel and Joubert syndromes. 11. Bardet-Biedel, and Jeune Syndromes. 12. Congenital disorder of glycosylation and their effects on the liver. 13. Autosomal recessive polycystic kidney disease. 14. Caroli disease, Caroli syndrome, and congenital hepatic fibrosis. 15. Simple hepatic cysts/ Choledochal cysts. 16. Autosomal dominant polycystic liver disease. 17. Echinococcal/Hydatid Cysts of the liver. 18. Miscellaneous cystic lesions of the liver
- D. Complications. 19. Vascular complications of fibrocystic liver disease. 20. Biliary cystadenoma and cystadenocarcinoma. 21. Cholangitis. G. Treatment. 22. Surgical Management of Fibrocystic Liver Disease.